EPILEPSY WITH MYOCLONIC ATONIC SEIZURES (EMAtS)

Mandatory seizures

Myoclonic-atonic seizures, myoclonic-atonic status epilepticus is common.

May have

• Febrile seizures
• Absence seizures - seen in half of patients, typically with myoclonic jerks, facial myoclonia and atonia (not just loss of awareness)
• Atypical absence seizures
• Atonic seizures
• Myoclonic seizures
• Generalized tonic-clonic seizures
• Tonic seizures are rare and associated with worse prognosis
• Non convulsive status epilepticus is common, lasting hours to days, manifesting as cognitive impairment with frequent atypical absence, myoclonic and atonic seizures

Exclusionary

• Epileptic spasms
• Focal seizures