HEMICONVULSION-HEMIPLEGIA-EPILEPSY SYNDROME (HHE)

Imaging

MRI immediately following the status epilepticus demonstrates diffuse hemispheric signal abnormalities with T2 hyperintensity and restricted diffusion, predominantly of the subcortical white matter of the affected hemisphere. Edema of the affected hemisphere can be severe. Subsequently, atrophy of the affected hemisphere is seen. Hippocampal sclerosis is also commonly seen.